List of hepato-biliary diseases

Hepato-biliary diseases include liver diseases and biliary diseases. Their study is known as hepatology.

• Acute hepatitis A
• Acute hepatitis B
• Acute hepatitis C
• Acute hepatitis D – this is a superinfection with the delta-agent in a patient already infected with hepatitis B
• Acute hepatitis E
• Chronic viral hepatitis
• Other viral hepatitis viruses may exist but their relation to the disease is not firmly established like the previous ones (hepatitis F, GB virus C, hepatitis X)

• Hepatitis:
  • cytomegalovirus infection
  • herpesviral: herpes simplex infection
• Toxoplasmosis
• Hepatosplenic schistosomiasis
• Portal hypertension in schistosomiasis
• Liver disease in syphilis
• Epstein–Barr virus infection
• yellow fever virus infection
• rubella virus infection
• leptospirosis
• Echinococcosis
• Amoebiasis

• liver abscess
• autoimmune hepatitis
• primary biliary cholangitis (primary biliary cirrhosis)
• phlebitis of the portal vein
• granulomatous hepatitis
  • berylliosis
  • sarcoidosis
• nonalcoholic steatohepatitis (NASH)

This may cause fatty liver, hepatitis, fibrosis and sclerosis leading to cirrhosis and finally liver failure.

This includes mostly drug-induced hepatotoxicity, (DILI) which may generate many different patterns over liver disease, including

• cholestasis
• necrosis
• acute hepatitis and chronic hepatitis of different forms,
• cirrhosis
• Effects of Acetaminophen (Tylenol)
• other rare disorders like focal nodular hyperplasia, Hepatic fibrosis, peliosis hepatis and veno-occlusive disease.

Liver damage is part of Reye syndrome.

Malignant neoplasm of liver and intrahepatic bile ducts. The most frequent forms are metastatic malignant neoplasm of liver)

• liver cell carcinoma
  • hepatocellular carcinoma
  • hepatoma
• cholangiocarcinoma
• hepatoblastoma
• angiosarcoma of liver
• Kupffer cell sarcoma
• other sarcomas of liver

Benign neoplasm of liver include hepatic hemangiomas, hepatic adenomas, and focal nodular hyperplasia (FNH).

Chronic liver diseases like chronic hepatitis, chronic alcohol abuse or chronic toxic liver disease may cause

• liver failure and hepatorenal syndrome
• fibrosis and cirrhosis of liver

Cirrhosis may also occur in primary biliary cirrhosis. Rarely, cirrhosis is congenital.

• metabolic diseases (chapter E in ICD-10)
  • haemochromatosis
  • Wilson's disease
  • Gilbert's syndrome
  • Crigler–Najjar syndrome
  • Dubin–Johnson syndrome
  • Rotor syndrome

• chronic passive congestion of liver
• central haemorrhagic necrosis of liver
• infarction of liver
• peliosis hepatis
• veno-occlusive disease
• portal hypertension
• Budd–Chiari syndrome

• Congenital cystic disease of the liver
• Cysts caused by Echinococcus
• Polycystic liver disease

Amyloid degeneration of liver

• malignant neoplasm of the gallbladder
• malignant neoplasm of other parts of biliary tract
  • extrahepatic bile duct
  • ampulla of Vater
• cholelithiasis
• cholecystitis
• others (excluding postcholecystectomy syndrome), but including
  • other obstructions of the gallbladder (like strictures)
  • hydrops, perforation, fistula
  • cholesterolosis
  • biliary dyskinesia
• ICD-10 code K83: other diseases of the biliary tract:
  • cholangitis (including ascending cholangitis and primary sclerosing cholangitis)
  • obstruction, perforation, fistula of biliary tract (bile duct)
  • spasm of sphincter of Oddi
  • biliary cyst
  • biliary atresia

ICD-10 codes K70-K77: Liver Diseases [1]